Ventrikelseptumaneurysma als seltene klinische Manifestation des Marfan-Syndroms

Translated title of the contribution: Ventricular septum aneurysm as a rare clinical manifestation of Marfan's syndrome

U. Bauer, M. Bauer, H. Siniawski, H. Gülmez, Friedrich D Knollmann, P. E. Lange, R. Hetzer

Research output: Contribution to journalArticle

Abstract

This is the first description of a patient with Marfan syndrome and an aneurysm of the ventricular septum. Apart from a borderline dilatation of the ascending aorta, there were no cardiovascular manifestations of Marfan syndrome. A transesophageal echocardiographic examination showed a large aneurysm of the ventricular septum. To prevent the imminent rupture and the acute occurrence of a significant left-to-right shunt on the ventricular level, as well as increasing irritation of tricuspid valve, an elective operation was performed. In patients with Marfan syndrome, besides the routine cardiological diagnostics, a search for intracardial defects is also necessary.

Original languageGerman
Pages (from-to)77-80
Number of pages4
JournalZeitschrift fur Herz-, Thorax- und Gefasschirurgie
Volume18
Issue number2
DOIs
StatePublished - Apr 2004
Externally publishedYes

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Keywords

  • Congenital heart defects
  • Marfan syndrome
  • Ventricular septum aneurysm

ASJC Scopus subject areas

  • Cardiology and Cardiovascular Medicine

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