Lymphangioleiomyomatosis and SZ α1-antitrypsin disease: A unique combination?

Andrew Chan, Sunye Kwack, Kirk D. Jones, Marilyn K. Glassberg, Charles R. Gherman

Research output: Contribution to journalArticlepeer-review

6 Scopus citations


We deseribe a case of a 37-year-old female ex-smoker with lymphangioleiomyomatosis and SZ α1-antitrypsin disease who underwent successful bilateral sequential lung transplantation. While this disease combination has not been described previously, we recommend vigilance for the possibility of sueh combinations in patients with chronic lung disease. The possible mechanisms of interaction resulting from both disease processes are discussed.

Original languageEnglish (US)
Pages (from-to)763-765
Number of pages3
Issue number2
StatePublished - Aug 1 2003


  • Chylothorax
  • COPD
  • Lymphangioleiomyomatosis
  • Matrix metalloproteinase
  • SZ α-antitrypsin disease

ASJC Scopus subject areas

  • Pulmonary and Respiratory Medicine


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