Lymphangioleiomyomatosis and SZ α1-antitrypsin disease: A unique combination?

Andrew Chan, Sunye Kwack, Kirk D. Jones, Marilyn K. Glassberg, Charles R. Gherman

Research output: Contribution to journalArticle

5 Scopus citations

Abstract

We deseribe a case of a 37-year-old female ex-smoker with lymphangioleiomyomatosis and SZ α1-antitrypsin disease who underwent successful bilateral sequential lung transplantation. While this disease combination has not been described previously, we recommend vigilance for the possibility of sueh combinations in patients with chronic lung disease. The possible mechanisms of interaction resulting from both disease processes are discussed.

Original languageEnglish (US)
Pages (from-to)763-765
Number of pages3
JournalChest
Volume124
Issue number2
DOIs
StatePublished - Aug 1 2003

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Keywords

  • Chylothorax
  • COPD
  • Lymphangioleiomyomatosis
  • Matrix metalloproteinase
  • SZ α-antitrypsin disease

ASJC Scopus subject areas

  • Pulmonary and Respiratory Medicine

Cite this

Chan, A., Kwack, S., Jones, K. D., Glassberg, M. K., & Gherman, C. R. (2003). Lymphangioleiomyomatosis and SZ α1-antitrypsin disease: A unique combination? Chest, 124(2), 763-765. https://doi.org/10.1378/chest.124.2.763