Linear nevus sebaceous syndrome

Alan M. Roth, John L Keltner

Research output: Contribution to journalArticlepeer-review

9 Scopus citations


The pathologic terms hamartoma, choristoma, nevus, and phakoma often are confused. We discuss them in relation to a patient with the linear nevus sebaceous syndrome who had a large limbal mass that grew unusually rapidly and was excised. Histopathologic examination showed that it was a complex choristoma composed of lacrimal gland, adipose tissue, and myxomatous tissue. The latter has not been described previously in this disorder. This neuro-oculocutaneous syndrome has been considered one of the phakomatoses.

Original languageEnglish (US)
Pages (from-to)44-49
Number of pages6
JournalJournal of Clinical Neuro-Ophthalmology
Issue number1
StatePublished - 1993


  • Adipose tissue
  • Complex choristoma
  • Conjunctiva
  • Lacrimal gland
  • Myxoma
  • Nevus sebaceus
  • Phakomatosis

ASJC Scopus subject areas

  • Clinical Neurology
  • Ophthalmology


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