Extra-abdominal fibromatosis (desmoid tumor) arising in the infratemporal fossa

A case report

Martin Corsten, Paul J. Donald, Arun Cadre, Regina F Gandour-Edwards, William Nemzek

Research output: Contribution to journalArticle

Abstract

Fibromatosis (or desmoid tumor) refers to a histologically benign but locally aggressive lesion arising from musculoaponeurotic structures in various anatomic sites. The lesion arises most commonly in the abdomen; the head and neck is the site of origin in only about 10-15% of extra-abdominal fibromatosis. We report a 26-year-old male patient who presented with progressive severe trismus and a left abducens palsy. Radiographs and biopsy confirmed the presence of diffuse fibromatosis at the left skull base, arising in the infratemporal fossa with significant intraand extracranial extension. A two-stage infra temporal fossa/middle cranial fossa resection failed to completely excise the tumor, which was found to extend to the contralateral cavernous sinus and skull base. A discussion of extra-abdominal fibromatosis, with review of the pathologic and radiologie findings in this case, is presented.

Original languageEnglish (US)
Pages (from-to)8
Number of pages1
JournalSkull Base Surgery
Volume8
Issue numberSUPPL. 1
StatePublished - 1998

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Abdominal Fibromatosis
Aggressive Fibromatosis
Fibroma
Skull Base
Middle Cranial Fossa
Trismus
Cavernous Sinus
Abdomen
Neoplasms
Neck
Head
Biopsy

ASJC Scopus subject areas

  • Clinical Neurology

Cite this

Extra-abdominal fibromatosis (desmoid tumor) arising in the infratemporal fossa : A case report. / Corsten, Martin; Donald, Paul J.; Cadre, Arun; Gandour-Edwards, Regina F; Nemzek, William.

In: Skull Base Surgery, Vol. 8, No. SUPPL. 1, 1998, p. 8.

Research output: Contribution to journalArticle

Corsten, Martin ; Donald, Paul J. ; Cadre, Arun ; Gandour-Edwards, Regina F ; Nemzek, William. / Extra-abdominal fibromatosis (desmoid tumor) arising in the infratemporal fossa : A case report. In: Skull Base Surgery. 1998 ; Vol. 8, No. SUPPL. 1. pp. 8.
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