Bilateral renal carcinoma in Von Hippel-Lindau disease

Edward M. Mullin, Ralph W deVere White, Lloyd J. Peterson, David F. Paulson

Research output: Contribution to journalArticle

11 Citations (Scopus)

Abstract

Von Hippel-Lindau disease, one of the phakomatoses, is believed to be a disorder of mesodermal differentiation. Renal lesions, usually cysts or adenocarcinomas with an occasional hemangioblastoma, occur in approximately two thirds of all patients. The renal neoplasms previously reported have been multiple, bilateral, and usually beyond resection. A thirty-eight-year-old white male with a cerebellar hemangioblastoma and bilateral renal adenocarcinoma underwent suboccipital craniotomy, right heminephrectomy, and left radical nephrectomy. No evidence of recurrent disease can be identified ten months postoperatively. An aggressive approach in this systemic disease appears to be warranted.

Original languageEnglish (US)
Pages (from-to)475-478
Number of pages4
JournalUrology
Volume8
Issue number5
DOIs
StatePublished - 1976
Externally publishedYes

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Hemangioblastoma
von Hippel-Lindau Disease
Nephrectomy
Neurocutaneous Syndromes
Carcinoma
Kidney
Craniotomy
Kidney Neoplasms
Renal Cell Carcinoma
Cysts
Adenocarcinoma

ASJC Scopus subject areas

  • Urology

Cite this

Bilateral renal carcinoma in Von Hippel-Lindau disease. / Mullin, Edward M.; deVere White, Ralph W; Peterson, Lloyd J.; Paulson, David F.

In: Urology, Vol. 8, No. 5, 1976, p. 475-478.

Research output: Contribution to journalArticle

Mullin, Edward M. ; deVere White, Ralph W ; Peterson, Lloyd J. ; Paulson, David F. / Bilateral renal carcinoma in Von Hippel-Lindau disease. In: Urology. 1976 ; Vol. 8, No. 5. pp. 475-478.
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